Foregut duplication cyst: a novel computed tomography finding mimicking a small bowel hernia: A case report.

RATIONALE: A foregut duplication cyst (FDC) is an uncommon congenital disease. This report presents a case of mediastinal foregut duplication cyst that mimicked a diaphragmatic small bowel hernia. PATIENT CONCERN: A 27-month-old girl was first referred for a mediastinal lesion found incidentally on a chest radiograph. At that time, our impression was cystic lung lesion such as congenital pulmonary airway malformation or pulmonary sequestration. At the age 6 years, she presented with recurrent vomiting. The physical examination and laboratory studies were within normal limits. DIAGNOSES: Chest CT revealed a thin- and smooth-walled cystic mass containing an air-fluid level in the left paravertebral space. It had several inner circular folds and characteristic double-layer enhancement and inner circular fold. Our radiological impression was a type I congenital cystic adenomatoid malformation. INTERVENTIONS: The patients undergone video-assisted thoracoscopic surgery for excision. The operative finding was the cystic mass with smooth bowel-like outer surface and located between the aorta and heart. The cyst was excised and confirmed to be a foregut duplication cyst pathologically. OUTCOMES: The patient was doing well with no postoperative complications during follow-up. Recurrent vomiting was improved. This is the first case report describing foregut duplication cyst mimicking a small bowel hernia. LESSONS: Foregut duplication cysts are rare congenital anomalies of primitive foregut origin. They can occur at any level of the alimentary track and comprise approximately 10% of all mediastinal tumors. Its characteristic double-layered histopathological nature, an FDC can show a double-layered enhancement pattern, which is typical in the alimentary tract.

Infected Congenital Epicardial Cyst Presenting as Acute Abdomen.

A previously healthy 3-year-old boy presented to the emergency department with abdominal pain, fever, and emesis. Laboratory and radiologic evaluation for causes of acute abdomen were negative; however, review of the abdominal x-ray demonstrated cardiomegaly with the subsequent diagnosis of pericardial cyst by echocardiogram and computed tomography. The patient underwent surgical decompression and attempted removal of the cystic structure revealing that the cyst originated from the epicardium. His abdominal pain and fever resolved postoperatively and he completed a 3-week course of ceftriaxone for treatment of Propionibacterium acnes infected congenital epicardial cyst. Emergency department physicians must maintain a broad differential in patients with symptoms of acute abdomen to prevent complications from serious cardiac or pulmonary diseases that present with symptoms of referred abdominal pain.

Achado Radiológico de Cisto Pericárdico / Radiologic Finding of Pericardial Cyst

Mulher de 46 anos de idade, em acompanhamento porinfecção cutânea por Bukhoderia pseudomallei em membrosuperior esquerdo, realizou radiografia de tórax para descartaracometimento pulmonar, que evidenciou hipotransparênciaem lobo inferior esquerdo (Figura 1A). Posteriormente, foisubmetida a tomografia de tórax que demonstrou coleçãolíquida, sem realce pelo meio de contraste, medindo 8cm no maior eixo axial, ocupando o seio cardiofrênicoesquerdo (Figura 1B). O ecocardiograma transtorácico (ECO)mostrou função sistólica preservada (FE 62% pelo Teichholz),espessamento pericárdico discreto e cisto pericárdico emregião posterior e em ponta do coração, contendo traves defibrina (Figura 2). Posteriormente, a paciente foi submetidaa drenagem percutânea do cisto guiada por US (citologia:hemácias 0, leucócitos 1.000, 60% mononucleares e 40%neutrófilos; cultura negativa). O ECO realizado um mês apósa drenagem demonstrou discreto espessamento pericárdico(4 mm) e ausência de derrame pericárdico. Paciente segueem tratamento ambulatorial com o infectologista.Cistos pericárdicos são anomalias congênitas raras egeralmente benignas. Representam 6% das massas mediastinaise 33% de todos os cistos do mediastino. A grande maioriados cistos é assintomática e geralmente é achado incidentalem exames de imagens que podem ser confundidos comaneurisma da artéria coronariana, neoplasias e pneumonia.Complicações como a ruptura do cisto, compressão cardíacae até mesmo morte súbita já forma descritas, porém sãoincomuns. Pode-se adotar uma conduta conservadora emcasos assintomáticos desde que seja possível o seguimentodo paciente, de forma a garantir um curso benigno em que ocisto pericárdico pode involuir espontaneamente...

Inflammation and Rupture of a Congenital Pericardial Cyst Manifesting Itself as an Acute Chest Pain Syndrome.

We present the case of a 63-year-old woman with a remote history of supraventricular tachycardia and hyperlipidemia, who presented with recurrent episodes of acute-onset chest pain. An electrocardiogram showed no evidence of acute coronary syndrome. A chest radiograph revealed a prominent right-sided heart border. A suspected congenital pericardial cyst was identified on a computed tomographic chest scan, and stranding was noted around the cyst. The patient was treated with nonsteroidal anti-inflammatory drugs, and the pain initially abated. Another flare-up was treated similarly. Cardiac magnetic resonance imaging was then performed after symptoms had resolved, and no evidence of the cyst was seen. The suspected cause of the patient's chest pain was acute inflammation of a congenital pericardial cyst with subsequent rupture and resolution of symptoms.

An unusual cause of stridor in an adult: mediastinal foregut duplication cyst.

We present a case of unusual presentation of stridor in an adult man who was identified to have a sudden expansion of a foregut duplication cyst in the mediastinum. This resulted in superior vena caval obstruction and subsequent airway compromise. Following resuscitation, the cyst was surgically removed via a thoracotomy which confirmed the diagnosis and provided definitive management. Foregut duplication cysts are an unusual cause of stridor in adults, with only five cases ever documented worldwide in the literature, presenting in such a manner. This case is a reminder of the importance of thorough clinical examination, the benefits of radiology as an indispensible adjunct and essential role of the multidisciplinary team.

Congenital cystic neck masses: embryology and imaging appearances, with clinicopathological correlation.

Congenital cystic masses of the neck are uncommon and can present in any age group. Diagnosis of these lesions can be sometimes challenging. Many of these have characteristic locations and imaging findings. The most common of all congenital cystic neck masses is the thyroglossal duct cyst. The other congenital cystic neck masses are branchial cleft cyst, cystic hygroma (lymphangioma), cervical thymic and bronchogenic cysts, and the floor of the mouth lesions including dermoid and epidermoid cysts. In this review, we illustrate the common congenital cystic neck masses including embryology, clinical findings, imaging features, and histopathological findings.

Double esophageal duplication cysts, with ectopic gastric mucosa: a case report.

Esophageal duplication cyst (EDC) is a congenital malformation of the posterior primitive foregut, which mainly occurs in the thoracic esophagus. Here, we describe a 3-year-old Han Chinese boy afflicted with intermittent fever of acute onset and dry cough. Thoracic computed tomography revealed an 10 cm × 5.4 cm × 5.8 cm oval-shaped, cyst-like tumor located in the extrapleural space, extending along the right paravertebral gutter and compressing the trachea forward. An additional small-sized, oval-shaped cyst was identified in the posterior mediastinum, between the esophagus and the spinal column, at the T1 level. During open thoracotomy, under general anesthesia, an opaque, thick-walled, esophageal cyst was revealed not to be in communication with the esophageal lumen or the trachea. This cyst was subsequently resected in an en bloc manner. The small (1-cm) esophageal cyst was left untreated based on a "wait-and-see" policy. Histological analysis showed that the resected cyst was walled by hyperplastic, fibrous tissues and locally lined with gastric mucosa inherent glands. This finding was consistent with a diagnosis of EDC, with ectopic gastric mucosa. The respiratory tract symptoms resolved immediately after the operation. Computed tomography obtained at the 6-month follow-up showed that no disease, residual or recurrence, was present after the resection of the large-sized cyst, and the small-sized cyst remained unchanged in size.

[Benign cysts of the mediastinum: series of 28 cases]. / Les kystes bénins du médiastin : à propos de 28 cas.

INTRODUCTION: Benign cystic mediastinal mass form a group of heterogeneous and uncommon lesions. Surgical resection is the gold standard in these conditions. We reported our institutional experience in management of these benign tumours. In this review, cardiac and ganglionary benign mass were excluded. METHODS: We retrospectively reviewed the records of 28 patients with benign cysts of the mediastinum, who are operated in our department between January 2003 and December 2009 (7years period). RESULTS: There were 13 females (46.4%) and 15 males (53.5%), with a mean age of 36.8years (range: 13-63years). Most lesions (n=22) were equally in the anterior and middle mediastinum, only six were in the posterior mediastinum. Seventeen patients (60.7%) were symptomatic, with chest pain and cough as the most common symptoms. The diagnosis of mediastinal cyst was fortuitous in 11 patients with the waning of an assessment made for another reason. Surgery was indicated in all patients in order to both diagnostic and therapeutic. Posterolateral thoracotomy incision is the most common. Complete resection of the cyst was possible only in 18 cases (64.3%), whereas in ten (35. 7%) other cases part of the cyst was left in place due to tight adhesions to vital structures. After histological study, there were: nine bronchogenic cysts (32.1%), seven hydatid cysts (25%), four cystic lymphangiomas (14.3%), three mature cystic teratomas (10.7%) and three pleuropericardial cysts, one thymic cyst and one parathyroid cyst. The postoperative course was uneventful and no recurrence has been observed until now. CONCLUSION: The benign cysts of the mediastinum is a rare entity, the hydatid etiology remains common in our context. Surgical treatment remains the treatment of choice for mediastinal cysts, when the patient is operable, to save the risk of complications or degeneration.

The tale of spring water cysts: a historical outline of surgery for congenital pericardial diverticula and cysts.

Congenital pericardial diverticula and cysts are extremely uncommon lesions within the anterior mediastinum. Both lesions derive from the pericardial celom and represent different stages of a common embryogenesis. Initial reports date from the 19th century. Surgical pioneers were Otto Pickhardt, who removed a pericardial cyst at Lenox Hill Hospital in New York in 1931, and Richard Sweet, who accomplished the first resection of a pericardial diverticulum at Massachusetts General Hospital in Boston in 1943. These lesions were also called spring water cysts because they usually contain watery, crystal-clear fluid. This history outlines the milestones of evolving surgical management, from the first report in 1837 up to the present time.

Congenital cystic lesions of the head and neck.

This article presents clinical characteristics and radiologic features of congenital cervical cystic masses, among them thyroglossal duct cysts, cystic hygromas, branchial cleft cysts, and the some of the rare congenital cysts, such as thymic and cervical bronchogenic cysts. The imaging options and the value of each for particular masses, as well as present clinical and radiologic images for each, are discussed.

Thymoma within a giant congenital thymic cyst.

Congenital thymic cysts are very rare and mostly asymptomatic mediastinal lesions. Thymoma within such cysts is even more uncommon and has so far hardly been described. We report on a 41-year-old male with a World Health Organization type B1 thymoma within the wall of a huge unilocular thymic cyst. Because of the possible coexistence of typical congenital thymic cyst and thymoma, we recommend surgical resection both for establishing the diagnosis and for definite treatment.

Congenital pericardial cyst in a naval special warfare candidate; clearance for diving after resection.

INTRODUCTION: We report the case of a 19-year-old male military recruit who presented for a screening physical for U.S. Naval Special Warfare and Diving Duty. During his screening physical examination, an exophytic pericardial cyst was discovered. Subsequent work-up revealed normal cardiopulmonary function despite this large 7-cm mass, but the candidate was disqualified due to concerns regarding the risk of complications. He underwent successful elective surgical resection without post-operative complications. One year post-operatively, he repeated his cardiopulmonary work-up with normal results and successfully completed training. METHODS: Literature search was conducted using PubMed/Medline. Keywords included pericardial/um, cyst, mediastinum, special operations, military, diving, thoracoscopy/ic resection. Results that included cases of pericardial cysts or other mediastinal tumors were included. RESULTS: Review of the literature reveals that complications are rare and range widely in severity. Analysis of the physiology of diving, together with absence of reported cases, suggest that there is little to no, increased risk in recreational scuba diving for subjects with asymptomatic lesions. While no cases of morbidity or mortality have been reported in elite athletes, the severe and repetitive trauma experienced by Special Operators raises clinical concern for these lesions. CONCLUSION: Because of the increased risk of morbidity and mortality in the Special Operations environment, clearance for duty should not be granted those individuals. However, in the general population, as well as with low-impact activities such as recreational scuba diving, periodic observation without resection seems reasonable.

Cervical ectopic thymic cyst: a rare preoperative diagnosis.

We present a case of a 5-year-old child with a painless swelling on the neck. Imaging revealed a multilocular cystic lesion lying in close proximity to carotid vessels. Based on imaging a possibility of ectopic thymic cyst was considered, which was confirmed on histopathology. Ectopic cervical cyst is an infrequent cause of neck cyst in a child which is rarely diagnosed preoperatively.

Large cervicothoracic thymic cyst causing prominent airway deviation in a 3-day-old neonate.

Cervicothoracic mass in the pediatric population is uncommon and has a broad differential diagnosis. Frequently, masses in the cervical region present with airway compromise, particularly in younger patients. We present a case of an extremely large cervicothoracic mass causing airway obstruction in a 3-day-old, otherwise healthy male infant. Following awake intubation for airway protection, a 4.5 cm x 2.5 cm x 1.5 cm thymic cyst was removed. This case illustrates the wide differential diagnosis of cervicothoracic masses and shows the difficulty of preoperative diagnosis, especially in the case of thymic cysts with extension into the cervical space.

Ectopic congenital thymic cyst in the right pleural cavity.

A 37-year-old man with a huge pleural cyst, presented with symptoms of right heart compression. The mass on the right side of the chest seemed initially to be in connection with the mediastinum. Computed tomography failed to define its relationship with the pericardium, and echocardiography excluded any involvement of the mediastinal structures. The final diagnosis was a congenital thymic cyst exclusively located in the pleural cavity.

Prenatal diagnosis of mediastinal neurentric cyst with an intraspinal component.

Mediastinal neurenteric cysts are the least common types of the bronchopulmonary foregut malformations, and their antenatal diagnosis is rare. We report a case of mediastinal neurenteric cyst diagnosed on antenatal ultrasonography at 28 weeks' gestation. A small intraspinal component and vertebral segmentation anomalies were also noted. The diagnosis was confirmed on postnatal magnetic resonance imaging and at the time of operation.

[Benign primary cystic lesions of mediastinum in adult: the clinical spectrum and surgical treatment]. / Lesiones quísticas primarias y benignas del mediastino en el adulto: espectro clínico y tratamiento quirúrgico.

BACKGROUND AND OBJECTIVE: The mediastinal cysts form a group of heterogeneous and uncommon benign lesions of neoplastic, congenital, or inflammatory conditions. The forgoing controversy is how to manage them; surgical removal or observation. We reviewed our experience including some rare conditions, emphasizing the clinical spectrum and surgical treatment. PATIENTES AND METHODS: This is a retrospective review between 2000 and 2007 included 34 cases of primary mediastinal cystic lesions. Clinical features, imaging techniques, surgical operation, morbidity, mortality and follow-up were analyzed. RESULTS: There were 18 females (53%) and 16 males (47%), with a mean age+/-standard deviation of 45.3+/-14.1 years (range: 22-74). Most of cysts were congenital (94%), except patients with hydatid disease (6%). 24% of cysts (n=8) were detected in anterior mediastinum. Rest of them (n=26) were located in visceral mediastinum. Patients usually were symptomatic (61%). Chest pain and discomfort was most common symptom, others were dyspnea, cough and hemoptysis, respectively. Cysts excision was performed in all cases with an uneventful recovery and with no recurrence in long term follow up. CONCLUSIONS: Asymptomatic mediastinal cysts are not rare. Surgery is a reliable method of treatment of mediastinal cysts with acceptable mortality and morbidity.

[The cysts and fistulas of the neck in material of Otolaryngology Department of Rydygier District Hospital in Cracow]. / Torbiele i przetoki szyi w materiale oddzialu Otolaryngologii Wojewódzkiego Szpitala Specjalistycznego im L. Rydygiera w Krakowie w latach 1997-2007.

The retrospective study describes 118 patients treated for congenital cysts and fistulas of the neck between 1997 and 2007 in ORL Department of Rydygier District Hospital in Cracow. Malformation was divided into midline and laterocervical region anomalies. Malformation of midline included thyreoglossal duct and dermoid cyst. The most common malformation of laterocervical were cysts followed by fistulas. The theory of development, method of diagnosis and operative management were presented. Complication and recurrences were rare. Proper differential diagnosis and radical operation led to successful cure.